{"id":7549,"date":"2022-11-22T13:00:22","date_gmt":"2022-11-22T10:00:22","guid":{"rendered":"https:\/\/urbancare.clinic\/fahrs-disease\/"},"modified":"2022-11-22T13:00:22","modified_gmt":"2022-11-22T10:00:22","slug":"maladie-de-fahr","status":"publish","type":"post","link":"https:\/\/urbancare.clinic\/fr\/fahrs-disease\/","title":{"rendered":"Maladie de Fahr"},"content":{"rendered":"<div><img decoding=\"async\" src=\"https:\/\/urbancare.clinic\/wp-content\/uploads\/2023\/02\/fahrs-disease.jpg\" class=\"ff-og-image-inserted\" style=\"display:none\"><\/div>\n<p><span class=\"highwire-journal-article-marker-start\"><\/span><\/p>\n<p id=\"p-1\">Un homme de 36 ans s&#039;est pr\u00e9sent\u00e9 avec des \u00e9tourdissements provoqu\u00e9s par la flexion depuis 2 mois. Il a d\u00e9crit la sensation de la pi\u00e8ce qui tournait sur elle-m\u00eame. Les \u00e9pisodes \u00e9taient brefs et duraient quelques secondes. Il a ni\u00e9 tout autre sympt\u00f4me. Il n\u2019y avait aucun ant\u00e9c\u00e9dent de traumatisme ou autre \u00e9v\u00e9nement d\u00e9clencheur. Son examen neurologique n\u2019a r\u00e9v\u00e9l\u00e9 aucun d\u00e9ficit moteur, sensoriel, de parole, de champ visuel ou cognitif. Les nerfs cr\u00e2niens et la fonction c\u00e9r\u00e9belleuse \u00e9taient intacts. Il n\u2019y avait pas de d\u00e9viation du regard ni de nystagmus. Les signes vitaux orthostatiques \u00e9taient n\u00e9gatifs. Un scanner de la t\u00eate a montr\u00e9 de vastes calcifications intracr\u00e2niennes bilat\u00e9rales sym\u00e9triques impliquant les noyaux gris centraux, le thalamus, les noyaux dent\u00e9s et sous-corticaux\u2026 <\/p>\n<p><span class=\"highwire-journal-article-marker-end\"><\/span><a href=\"http:\/\/pmj.bmj.com\/cgi\/content\/short\/98\/1166\/e39?rss=1\">Source quotidienne m\u00e9dicale<\/a><\/p>\n<p>","protected":false},"excerpt":{"rendered":"<p>Un homme de 36 ans a pr\u00e9sent\u00e9 des vertiges depuis 2 mois provoqu\u00e9s par la flexion. Il a d\u00e9crit la sensation que la pi\u00e8ce tournait autour de lui. Les \u00e9pisodes \u00e9taient brefs et ont dur\u00e9 quelques secondes. Il a ni\u00e9 tout autre sympt\u00f4me. Il n&#039;y avait aucun ant\u00e9c\u00e9dent de traumatisme ou autre \u00e9v\u00e9nement d\u00e9clencheur. Son examen neurologique n&#039;a montr\u00e9 aucun d\u00e9ficit moteur, sensoriel, de la parole, du champ visuel ou cognitif. Les nerfs cr\u00e2niens et la fonction c\u00e9r\u00e9belleuse \u00e9taient intacts. Il n&#039;y avait pas de d\u00e9viation du regard ni de nystagmus. Les signes vitaux orthostatiques \u00e9taient n\u00e9gatifs. Un scanner de la t\u00eate a montr\u00e9 des calcifications intracr\u00e2niennes bilat\u00e9rales sym\u00e9triques \u00e9tendues impliquant les noyaux gris centraux, le thalamus, les noyaux dent\u00e9s et la substance blanche sous-corticale du cerveau, y compris l&#039;implication des lobes frontaux, temporaux, pari\u00e9taux et occipitaux ainsi que du m\u00e9senc\u00e9phale et du pont (<cross-ref type=\"fig\" refid=\"F1\">figures 1 \u00e0 3<\/cross-ref><cross-ref type=\"fig\" refid=\"F2\"><\/cross-ref><cross-ref type=\"fig\" refid=\"F3\"><\/cross-ref>) compatible avec la maladie de Fahr. Une discussion d\u00e9taill\u00e9e de la maladie affectant d&#039;autres membres de la famille s&#039;est av\u00e9r\u00e9e n\u00e9gative. Un\u2026<\/p>","protected":false},"author":2,"featured_media":7550,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"Default","format":"standard","meta":{"page_builder":"","fifu_image_url":"https:\/\/urbancare.clinic\/wp-content\/uploads\/2023\/02\/fahrs-disease.jpg","fifu_image_alt":"","footnotes":""},"categories":[185],"tags":[],"class_list":["post-7549","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-research-medical-articles"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v28.4 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Fahrs disease - Urban Care Clinic<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/urbancare.clinic\/fr\/maladie-de-fahr\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Fahrs disease - Urban Care Clinic\" \/>\n<meta property=\"og:description\" content=\"A 36-year-old man presented with a 2-month history of dizziness brought on with bending. He described the sensation of the room spinning around. The episodes were brief and lasted a few seconds. He denied any other symptoms. There was no history of trauma or other precipitating event. His neurological examination showed no motor, sensory, speech, visual field or cognitive deficit. Cranial nerves and cerebellar function were intact. There was no gaze deviation or nystagmus present. Orthostatic vital signs were negative. A CT scan of the head showed extensive bilateral symmetric intracranial calcifications involving the basal ganglia, thalamus, dentate nuclei and subcortical white matter of the cerebrum including involvement of both frontal, temporal, parietal and occipital lobes as well as the midbrain and pons (figures 1&ndash;3) consistent with Fahr&#039;s disease. A detailed discussion of the condition affecting any other family members was negative. An...\" \/>\n<meta property=\"og:url\" content=\"https:\/\/urbancare.clinic\/fr\/maladie-de-fahr\/\" \/>\n<meta property=\"og:site_name\" content=\"Urban Care Clinic\" \/>\n<meta property=\"article:publisher\" content=\"https:\/\/www.facebook.com\/urbancarezanzibar\" \/>\n<meta property=\"article:published_time\" content=\"2022-11-22T10:00:22+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/urbancare.clinic\/wp-content\/uploads\/2023\/02\/fahrs-disease.jpg\" \/>\n\t<meta property=\"og:image:width\" content=\"1024\" \/>\n\t<meta property=\"og:image:height\" content=\"1024\" \/>\n\t<meta property=\"og:image:type\" content=\"image\/jpeg\" \/>\n<meta name=\"author\" content=\"Urban Care Clinic\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"\u00c9crit par\" \/>\n\t<meta name=\"twitter:data1\" content=\"Urban Care Clinic\" \/>\n\t<meta name=\"twitter:label2\" content=\"Dur\u00e9e de lecture estim\u00e9e\" \/>\n\t<meta name=\"twitter:data2\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\\\/\\\/schema.org\",\"@graph\":[{\"@type\":\"Article\",\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/fahrs-disease\\\/#article\",\"isPartOf\":{\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/fahrs-disease\\\/\"},\"author\":{\"name\":\"Urban Care Clinic\",\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/#\\\/schema\\\/person\\\/a304a61bcf298680ee41e2e9ae193930\"},\"headline\":\"Fahrs disease\",\"datePublished\":\"2022-11-22T10:00:22+00:00\",\"mainEntityOfPage\":{\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/fahrs-disease\\\/\"},\"wordCount\":106,\"publisher\":{\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/#organization\"},\"image\":{\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/fahrs-disease\\\/#primaryimage\"},\"thumbnailUrl\":\"https:\\\/\\\/urbancare.clinic\\\/wp-content\\\/uploads\\\/2023\\\/02\\\/fahrs-disease.jpg\",\"articleSection\":[\"Research Articles\"],\"inLanguage\":\"fr-FR\"},{\"@type\":\"WebPage\",\"@id\":\"https:\\\/\\\/urbancare.clinic\\\/fahrs-disease\\\/\",\"url\":\"https:\\\/\\\/urbancare.clinic\\\/fahrs-disease\\\/\",\"name\":\"Fahrs disease - 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