{"id":7703,"date":"2023-03-27T10:59:52","date_gmt":"2023-03-27T07:59:52","guid":{"rendered":"https:\/\/urbancare.clinic\/what-is-fowlers-syndrome-rare-condition-leaves-woman-unable-to-normally-urinate\/"},"modified":"2023-03-27T10:59:52","modified_gmt":"2023-03-27T07:59:52","slug":"was-ist-das-fowlers-syndrom-eine-seltene-erkrankung-fuhrt-dazu-dass-eine-frau-nicht-normal-urinieren-kann","status":"publish","type":"post","link":"https:\/\/urbancare.clinic\/de\/was-ist-das-fowlers-syndrom-eine-seltene-erkrankung-fuhrt-dazu-dass-eine-frau-nicht-normal-urinieren-kann\/","title":{"rendered":"Was ist das Fowler-Syndrom? Eine seltene Erkrankung f\u00fchrt dazu, dass eine Frau nicht normal urinieren kann"},"content":{"rendered":"<div><img decoding=\"async\" src=\"https:\/\/urbancare.clinic\/wp-content\/uploads\/2023\/03\/what-is-fowlers-syndrome-rare-condition-leaves-woman-unable-to-normally-urinate.jpg\" class=\"ff-og-image-inserted\" style=\"display:none\"><\/div>\n<p>Eine 30-j\u00e4hrige Frau in Gro\u00dfbritannien, die mehr als ein Jahr lang nicht in der Lage war, normal zu urinieren, hat in den sozialen Medien von ihrem Leidensweg berichtet und erkl\u00e4rt, dass es 14 Monate gedauert habe, bis sie eine Diagnose \u00fcber ihre seltene Erkrankung erhalten habe.<\/p>\n<p>Die Krankheit, die Elle Adams aus Ost-London betraf, f\u00fchrte dazu, dass sie nicht pinkeln konnte, obwohl sie viel Fl\u00fcssigkeit trank und den Drang versp\u00fcrte, zu urinieren.<\/p>\n<p>\u201eIch war \u00e4u\u00dferst gesund. Ich hatte keine anderen Probleme. Eines Tages bin ich aufgewacht und konnte nicht pinkeln\u201c, sagte Adams <a href=\"https:\/\/www.livemint.com\/science\/health\/30-year-old-from-uk-unable-to-pee-for-14-months-gets-rare-disease-affecting-young-women-fowler-syndrome-11679747702136.html\" target=\"_blank\" rel=\"noopener\">genannt<\/a> auf ihrer Seite. \u201eIch war sehr besorgt. Ich befand mich an einem Bruchpunkt \u2013 mein Leben hatte sich v\u00f6llig ver\u00e4ndert. Ich war nicht in der Lage, eine einfache Aufgabe wie den Toilettengang zu erledigen\u201c, f\u00fcgte sie hinzu.<\/p>\n<p>Obwohl die \u00c4rzte ihren Zustand zun\u00e4chst nicht diagnostizieren konnten, wurde ihr fast 14 Monate sp\u00e4ter mitgeteilt, dass sie am Fowler-Syndrom leide. Die \u00c4rzte warnten sie auch davor, dass sie aufgrund der seltenen Erkrankung f\u00fcr den Rest ihres Lebens einen Katheter verwenden m\u00fcsste.<\/p>\n<p>\u201eIch geh\u00f6re zu den Tausenden Frauen, deren Leben durch das Fowler-Syndrom zerst\u00f6rt wurde\u201c, sagte Adams und f\u00fcgte hinzu, dass viele Menschen sich der Erkrankung immer noch nicht bewusst seien.<\/p>\n<p><strong>Was ist das Fowler-Syndrom?<\/strong><\/p>\n<p>Fowler-Syndrom <a href=\"https:\/\/rarediseases.info.nih.gov\/diseases\/2365\/fowlers-syndrome\" target=\"_blank\" rel=\"noopener\">wirkt<\/a> junge Frauen im Alter zwischen 20 und 30 Jahren. Die Erkrankung \u00e4u\u00dfert sich in der Regel ohne weitere Symptome au\u00dfer der Unf\u00e4higkeit, die Blase zu entleeren. Bei manchen Frauen kann es jedoch zu R\u00fcckenschmerzen, suprapubischen Schmerzen und Unwohlsein aufgrund von Harnwegsinfektionen kommen.<\/p>\n<p>Sie entsteht, wenn sich der \u00e4u\u00dfere Harnr\u00f6hrensphinkter nicht entspannt und der Urin nicht normal abflie\u00dfen kann.<\/p>\n<p>Der Harnr\u00f6hrensphinkter ist eine Muskelstruktur <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK482438\/#:~:text=The%20internal%20urethral%20sphincter%20regulates,the%20bladder%20to%20the%20urethra.\" target=\"_blank\" rel=\"noopener\">regelt<\/a> der Abfluss von Urin aus der Blase in die Harnr\u00f6hre. W\u00e4hrend der innere Harnr\u00f6hrenschlie\u00dfmuskel den unwillk\u00fcrlichen Urinfluss von der Blase zur Harnr\u00f6hre steuert, reguliert der \u00e4u\u00dfere Harnr\u00f6hrenschlie\u00dfmuskel die willk\u00fcrliche Kontrolle des Urins von der Blase zur Harnr\u00f6hre.<\/p>\n<p>Der <a href=\"https:\/\/www.medicaldaily.com\/what-aquagenic-urticaria-rare-condition-makes-child-allergic-water-422695\">selten<\/a> Zustand ist <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/pmc\/articles\/PMC8005021\/\" target=\"_blank\" rel=\"noopener\">gesch\u00e4tzt<\/a> in 0,2 F\u00e4llen pro 100.000 Menschen pro Jahr auftreten.<\/p>\n<p>Obwohl die genaue Ursache des Schlie\u00dfmuskelversagens unbekannt ist, tritt es bei Frauen meist spontan oder nach einem chirurgischen Eingriff, einer Geburt, Opiatkonsum oder einer anderen Erkrankung auf.<\/p>\n<p>Der Schweregrad der Erkrankung variiert bei jedem Patienten. Bei manchen Patienten f\u00e4llt es m\u00f6glicherweise schwer, Urin zu lassen, wobei erhebliche Mengen zur\u00fcckgehalten werden, w\u00e4hrend andere unter einer v\u00f6lligen Retention leiden. Wer keine vollst\u00e4ndige Retention hat, kann wiederkehrende Blasenentz\u00fcndungen oder sogar Niereninfektionen bemerken.<\/p>\n<p><strong>Welche Behandlungsm\u00f6glichkeiten gibt es?<\/strong><\/p>\n<p>Die Behandlungsm\u00f6glichkeiten richten sich nach der Schwere der Erkrankung und der nach dem Wasserlassen verbleibenden Urinmenge. Bei Patienten mit sehr geringen Restvolumina ist kein Eingriff erforderlich, w\u00e4hrend bei Patienten mit hohen Restvolumina eine regelm\u00e4\u00dfige intermittierende Katheterisierung erforderlich ist.<\/p>\n<p>In schweren F\u00e4llen ben\u00f6tigen Patienten mit vollst\u00e4ndiger Retention m\u00f6glicherweise eine Sakralnervenstimulation (SNS). <a href=\"https:\/\/www.cincinnatichildrens.org\/service\/c\/colorectal\/treatments\/sacral-nerve-stimulation#:~:text=It%20delivers%20gentle%20electrical%20impulses,bladder%20muscles%20to%20work%20normally.\" target=\"_blank\" rel=\"noopener\">Therapie<\/a>Dabei werden sanfte elektrische Impulse \u00fcber eine Sonde abgegeben, die in der N\u00e4he des Sakralnervs platziert wird.<\/p>\n<p> \u201eEs ist nicht lebensver\u00e4ndernd, aber es kann helfen. Ich katheterisiere viel seltener, etwa 50% weniger. Es hat mein Leben einfacher gemacht, nach zwei Jahren der H\u00f6lle ist es alles, was ich mir w\u00fcnschen kann\u201c, sagte Adams, der sich der Therapie im Januar 2023 unterzog.<\/p>\n<p>Ver\u00f6ffentlicht von Medicaldaily.com<\/p>\n<p><a href=\"https:\/\/www.medicaldaily.com\/what-fowlers-syndrome-rare-condition-leaves-woman-unable-normally-urinate-469165\">Medizinische t\u00e4gliche Quelle<\/a><\/p>\n<p>","protected":false},"excerpt":{"rendered":"<p>Die seltene Erkrankung, die Elle Adams aus dem Osten Londons betraf, f\u00fchrte dazu, dass sie nicht pinkeln konnte, obwohl sie viel Fl\u00fcssigkeit trank und den Drang versp\u00fcrte, zu urinieren.<\/p>","protected":false},"author":2,"featured_media":7704,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"Default","format":"standard","meta":{"fifu_image_url":"https:\/\/urbancare.clinic\/wp-content\/uploads\/2023\/03\/what-is-fowlers-syndrome-rare-condition-leaves-woman-unable-to-normally-urinate.jpg","fifu_image_alt":"","footnotes":""},"categories":[27],"tags":[],"class_list":["post-7703","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-blog"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.6 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>What Is Fowler&#039;s Syndrome? 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